Abstracto

Euro Dentistry Congress 2019: A case report: Papillon Lefevre Syndrome - Rumeysa Cihangir - Istanbul University

 Rumeysa Cihangir 

 Aim: This article aims to present an advanced therapeutic approach based entirely on adhesive dentistry.   Objective: Papillon Lefevre Syndrome (PLS) is an autosomal recessive inherited genetic disorder characterized by palmoplantar hyperkeratosis and premature loss of deciduous and permanent teeth. Mutation of cathepsin C gene has been detected in the patient with PLS. In this case report, oral and radioghaphic findings of one PLS patient were discussed. 

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